Lung and chest wall volume during vital capacity manoeuvre in Osteogenesis Imperfecta
Abstract Background Although Osteogenesis Imperfecta (OI) affects the connective tissue, pulmonary function might be compromised because of thoracic deformities.OI is known to be a restrictive lung disease, but spirometry provides global measurement without localizing the site of the restriction.Opto-electronic plethysmography (OEP), is a non-invas